First European case of TAFRO syndrome associated with Sjogren disease
نویسندگان
چکیده
We herein describe a case of an unusual multicentric castleman disease(MCD) accompanied by Thrombocytopenia, Anasarca, myeloFibrosis and Renal failure, compatible with TAFRO syndrome and associated with Sjogren disease. The treatment with corticosteroids dramatically improved the symptoms. The clinical features of this case were similar to those reported previously in Japan but this appears to be the first European MCD with negative HHV8 and HIV that meets the criteria of TAFRO syndrome, associated with Sjögren disease.
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